Macrodystrophia Lipomatosa: A Single Large Radiological Study of a Rare Entity
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چکیده
منابع مشابه
Macrodystrophia Lipomatosa: A rare presentation
Macrodystrophia lipomatosa is a rare congenital nonhereditary mesenchymal hamartomatous malformation resulting in localized gigantism of parts of extremities that manifests clinically as macrodactyly or megalodactyly. Radiological and Pathological hallmark is the disproportionate fibroadipose tissue proliferation in subcutaneous tissue, nerve sheaths, and periosteum that leads to soft tissue an...
متن کاملMacrodystrophia Lipomatosa: Clinico-patho-radiological Correlation
Macrodystrophia lipomatosa is a rare congenital nonhereditary developmental anomaly. It is characterized by hamartomatous proliferation of the soft tissue leading to disproportionate enlargement of the limbs and digits. Since it leads to diagnostic dilemma, it has to be differentiated from various other conditions as they differ in course, prognosis, complications, and treatment. Herein, we pre...
متن کاملMacrodystrophia Lipomatosa
remaining three ulnar digits appeared normal. Magnetic resonance imaging (MRI) revealed characteristics of macrodystrophia lipomatosa such as enlargement and marked proliferation of the adipose tissues of the left hand, especially the radial aspect. MRI also demonstrated excessive fibrofatty tissue around the affected digits. This tissue has the same signal characteristics as fat on MRI, that i...
متن کاملA Review of Macrodystrophia Lipomatosa: Revisitation
Macrodystrophia lipomatosa (MDL) is a rare congenital non-hereditary disorder that has significant impact on patient morbidity. This study provides a comprehensive review of the natural history, diagnosis, management, and outcomes of the disorder. A literature search in PubMed was conducted to identify cases of MDL from January 1950 to 14 February 2014. After ruling out articles without informa...
متن کاملOn a case of "Macrodystrophia lipomatosa".
Macrodistrophia Lipomatosa is a congenital malformation of rare finding and unknown pathogenic mechanism. The pathology is mainly characterized by the interest of lower extremities and peculiar macroscopic feature is the presence of hyperthrophic fibro-adipose tissue. In our experience the localization to the upper extremities and the presence of uncommon clinical signs show the importance of i...
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ژورنال
عنوان ژورنال: Journal of Clinical Imaging Science
سال: 2019
ISSN: 2156-7514
DOI: 10.25259/jcis-9-4